Intrathoracic Malignant Peripheral Nerve Sheath Tumor in Neurofibromatosis 1

摘要

A 37-year-old man with a history of neurofibromatosis 1 presented to the hospital with a 3-day history of cough, pleuritic chest pain, and dyspnea. Physical examination showed tachycardia, tachy-pnea, normal oxygen saturation on room air, markedly decreased breath sounds with faint crackles in the right lung, multiple cutaneous neurofibromas, cafe au lait macules, and skinfold freckling#