A Diagnostic Pitfall: Atypical Teratoid Rhabdoid Tumor Versus Dedifferentiated/Poorly Differentiated Chordoma: Analysis of a Mono-institutional Series

摘要

Rhabdoid tumor (RT) was originally described in 1978 in the kidney as a variant of Wilms tumor with a rhabdosarcomatous component.1 RTs were successively reported in various anatomic sites including central nervous system (CNS). CNS's RT is referred as atypical teratoid (AT)/RT. It was reported for the first time in 1987 in a conference abstract,2 later denned as a distinct entity in 19963 and finally classified as an embryonal grade IV tumor by the World Health Organization classification of CNS tumors in 2000.4