Two-Stage Urethroplasty with Buccal Mucosa for Penoscrotal Hypospadias Reconstruction in a Male with a 46,XX Karyotype

摘要

We present a case regarding a 32-year old African male with penoscrotal hypospadias, left cryptorchidism and a left?inguinal hernia. There were moderate masculinization characteristics. He underwent a Lichtenstein hernia repair with?perioperative biopsies of the left inguinal testis and epididymis. Microscopic examination showed a Sertoli-only left?testis with Leydig-cell hyperplasia and the left epididymis consisted of ovarian tissue with corpora albicantia and?maturing follicles. Endocrinological evaluation showed a sex-determining region Y (SRY) negative 46,XX karyotype.?We successfully performed a two-stage urethroplasty with buccal mucosa graft to reconstruct his penoscrotal?hypospadias.