Sirolimus Decreases Circulating Lymphangioleiomyomatosis Cells in Patients With Lymphangioleiomyomatosis

摘要

Lymphangioleiomyomatosis (LAM), a rare multisystem disorder affecting primarily women of child-bearing age, is characterized by cystic lung destruction, lymphatic involvement (eg, chylous pleural effusions, lymphangioleiomyomas), and renal angiomyolipomas (AMLs).