cqvip:Introduction. Devic optic neuromyelitis is a rare clinical disease that invol ves severe transverse myelitis and unilateral or bilateral optic neuropathy. Its pathogenesis would be explained by demyelinization triggered by bacterial or vi ral infections phenomena. According to several author, prognosis would be better in children. Case report. We report a case of optic neuromyelitis in an 8-yea r-old child with an uneventful history who was admitted because he suffered fr om flaccid tetraplegia and sudden decline of the visual acuity. The ophthalmolog ic examination revealed bilateral neuropapillitis. The medullary MRI visualized a spreading myelitis with bifocal arachnoiditis. Search for a precipitating infe ctious factor showed positive IgM for viral hepatitis A. With corticosteroid tre atment the child achieved total recovery of vision and recovered motor and senso rial function of the upper limbs and the trunk. Paraplegia with sphincteral diso rders persisted. Conclusion. This case characterized by the precipitating factor (hepatitis virus A), illustrates this rare syndrome. We present a general revie w of the pediatric cases reported in the literature.
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