Carba-sugar amine derivative and glycolipid metabolic disorder treating agent containing the same as active ingredient

摘要

Methods for stabilizing β-galactosidase, stabilizing β-glucocerebrosidase, treating a glycolipid metabolic disorder caused by mutation of β-galactosidase gene, treating a glycolipid metabolic disorder caused by mutation of β-glucocerebrosidase gene, regenerating the activity of β-galactosidase, regenerating the activity of β-glucosidase, treating GM1 gangliosidosis, Morquio-B or Krabbe's disease, and treating Gaucher's disease, include administering a carba-sugar amine derivative represented by the following formula (1) or (2):;