Fat-forming variant of solitary fibrous tumour of the orbit: the entity previously known as lipomatous haemangiopericytoma.

摘要

The fat-forming variant of solitary fibrous tumour (SFT) previously known as lipomatous haemangiopericytoma is a distinctive soft tissue tumour composed of haemangiopericytoma-like areas interspersed with mature adipose tissue. Around 40 cases have been reported in the literature.1 These tumours usually occur in deep soft tissue and only three orbital cases have been described.1"3 Case report A 49-year-old woman presented with acute left eye pain, epiphora, and proptosis. There was a history of thyroid eye disease and bilateral proptosis that had required orbital decompression and low-dose radiotherapy 6 years previously.