Unilateral congenital malformations of middle ear with intact external ear: a review of 64 cases

摘要

Objective To describe the operative findings and surgical results of unilateral congenital middle ear malformations with intact external ear. Methods A retrospective review was performed on 64 patients with unilateral congenital middle ear malformations and intact external ear who underwent exploratory tympanotomy from 2011 to 2016. Demographic data, clinical data, high-resolution computed tomography findings, audiometric data and intraoperative findings were collected. Audiological evaluations before and 6?months after surgery were analyzed in 47 patients. Results The most common malformation were mobile stapes with missing incus long process and stapes suprastructure. The air conduction pure tone average was 58.9?±?10.5?dB HL (range 34.4–78.1?dB HL) preoperatively and 28.8?±?10.6?dB HL (range 9.4–55.6?dB HL) postoperatively ( P ?=?0.000). Twenty-five cases (53.2%) acquired an air conduction hearing gain exceeding 30?dB. Mean air-bone gap (ABG) was 44.5?±?9.4?dB (range 22.5–66.4?dB HL) before surgery and 15.6?±?9.3?dB (range 0–35.6?dB) after surgery ( P ?=?0.000) for an average gain of 28.8?±?11.5?dB. Thirty-four cases (72.3%) showed a postoperative ABG of less than 20?dB, 15 had an ABG within 10?dB, and 4 had 0?dB ABG after operation. No significant difference was observed for air conduction hearing gain regarding age ( P ?=?0.261) or types of malformations (mobile stapes footplate with or without a suprastructure anomaly, P ?=?0.058). Conclusion Unilateral congenital middle ear malformations with intact external ear can be complex and diverse. Functional ossiculoplasty for patients with unilateral congenital middle ear malformations can achieve good hearing outcomes.