Profound pectus excavatum in Marfan's syndrome

摘要

A 30- year-old man with Marian's syndrome and a family history of aortic dissection presented to our cardiovascular magnetic resonance (CMR) unit for assessment of his aorta because echocardiography had shown aortic root dilatation (46 mm). On examination, he had profound pectus excavatum (figure A). CMR showed levocardia (figure B) and severe costal recession (figure C); however, right ventricular dimensions and ejection fraction (figure D) were normal.