Classification of primary immunodeficiency diseases by the International Union of Immunological Societies (IUIS) Expert Committee on Primary Immunodeficiency 2011

摘要

Traditionally the International Union of Immunological Societies (IUIS) Expert Committee on Primary Immunodeficiency has revised the classification of primary immunodeficiency diseases (PIDs) every 2 years since 1973. The aim is to provide a document that not only demonstrates the scientific basis of these conditions, but assists clinicians in diagnosing patients with this rare group of diseases. In addition, the PID committee has recently advised, based on the latest tables, the revision of the World Health Organization International Disease (ICD) codes as relating to PIDs, due for publication in 2015. The ICDs form the basis on which funding for health care is provided in many, if not most, countries around the world, so the new classification has particular relevance for health-care providers this year.