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An extremely rare cause of generalized lymphadenopathy in children: Kimura's disease

机译:儿童广泛性淋巴结病的一种极为罕见的原因:木村氏病

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Kimura's disease, characterized by a triad of painless subcutaneous masses in the head and neck, prominent eosinophilia and markedly elevated immunoglobulin E levels, is an uncommon idiopathic, chronic inflammatory disease that usually affects young and middle-aged Asian males. Kimura's disease is known usually as a localized process and is an extremely rare cause of generalized lymphadenopathy in children. We report an eight-year-old Turkish boy with Kimura's disease who presented with generalized lymphadenopathy masquerading as malignant lymphoma.
机译:木村病以头部和颈部无痛的皮下组织三联征,嗜酸性粒细胞增多和免疫球蛋白E水平明显升高为特征,是一种罕见的特发性慢性炎症性疾病,通常会影响亚洲年轻和中年男性。木村病通常被称为局部过程,是儿童广泛性淋巴结病的极少原因。我们报告了一个八岁的木村病的土耳其男孩,他表现为全身淋巴结病,伪装成恶性淋巴瘤。

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