KARTAGENER?S SYNDROME PRESENTED AS PARANASAL POLYPOSIS WITH RECURRENT EPISTAXIS: A RARE CLINICAL CASE REPORT

摘要

Genetically determined syndromes of ciliary dyskinesia prevent normal transport of mucus from the bronchial tree to the mouth and result in serious impairment of lung defence system.male infertility was sometimes associated with Immotile spermatozoa. Approximately half of patients with Primary Ciliary Dyskinesia have full triad of kartgeners?s syndrome, give history of recurrent sinusitis and lower respiratory tract infection from early life to adulthood. Kartagener?s syndrome has been considered to be a sub group in a heterogenous collection of disorders to which Immotile Ciliary Syndrome or Dyskinitic cilia syndrome have been applied. There may also be a link with retinitis pigmentosa and hearing loss. Kartagener?s syndrome with paranasal polyposis is a uncommon presentation shown in our case. We report an adult female of 23 of age having Recurrent sinusitis,Bronchiectasis and Dextrocardia with Situs inversus and with Paranasal polyposis showing recurrent epistaxis. Conclusion: Kartagener?s syndrome with paranasal sinusitis is common but paranasal polyposis with epistaxis is uncommon way of presentation.