Case Report-Abdominal cocoon in identical twins: Is it congenital collagen tissue disorder? Report of two cases with review of literature

摘要

Abdominal cocoon (AC) is a rare disease entity most often found in adolescent girls from tropical and subtropical countries. The etiology is largely unknown. We report herein our experience of two cases of AC detected first time in identical female twins in the literature so far. One presented with acute intestinal obstruction and another asymptomatic one was evaluated on the basis of high index of suspicion and was operated for the same. Recovery was uneventful in both the cases. It is also hypothesized that the AC could be considered as congenital collagen tissue disorder, having some genetic predisposition. To the best of our knowledge, there are no reported cases within the same family. In addition, it has not been identified in subsequent generations, making a single gene mutation unlikely.