Isolated leptomeningeal angiomatosis in the sixth decade of life an adulthood variant of Sturge Weber Syndrome (Type III): role of advanced Magnetic Resonance Imaging and Digital Subtraction Angiography in diagnosis

摘要

CT (a), CTA (b-c) and MRI brain (d-f). Axial non-enhanced CT (a) shows hyperdense lesion in the right parietal convexity subarachnoid spaces (arrow) associated with hypo-attenuation of subcortical and deep white matter (white asterisk). Maximum Intensity Projection (b) and Volume Rendering (c) from CTA show no significant abnormalities. Axial T2-weighted Gradient Echo (GRE) (d) and Turbo Spin Echo (TSE) images (e) depict curvilinear hypointensity along the right parietal convexity (arrowheads) with hyperintense signal in underlying deep white matter (black asterisk) and subtle enlargement of lateral ventricle (white arrow). Postgadolinium axial Spin Echo (SE) T1-weighted image (f) shows intense serpentine leptomeningeal enhancement along the sulci and gyri of the right parietal lobe (white arrow)