Benefits of chronic blood transfusion in hemoglobin E/β thalassemia with pulmonary arterial hypertension

摘要

ObjectiveThe aim of the research reported here was to compare pulmonary artery systolic pressure (PASP) and 6-minute walk distance after 1 year of follow-up in hemoglobin E/β thalassemia (E/β-Thal) with pulmonary arterial hypertension (PAH) patients who received chronic blood transfusions versus those who received occasional transfusions.