019. Idiopathic interstitial pneumonias: clinico-radiologic-pathologic diagnosis

摘要

BackgroundThe idiopathic interstitial pneumonias (IIPs) represent a heterogeneous group of lung diseases with effects on the lung parenchyma and airways characterized by chronic inflammation and progressive fibrosis and share similar features (clinical, radiological). The idiopathic interstitial pneumonias are classified based on clinical, histopathological and radiological criteria in idiopathic pulmonary fibrosis-usual interstitial pneumonia (IPF-UIP), nonspecific interstitial pneumonia (NSIP), cryptogenic organizing pneumonia (COP), desquamative interstitial pneumonia (DIP), acute interstitial pneumonia (AIP), respiratory bronchiolitis-associated interstitial lung disease (RB-ILD) and lymphocytic interstitial pneumonia (LIP).