肺高血压指肺内循环系统发生高血压.伴或不伴有肺小动脉病变为特征的恶性肺血管疾病,往往引起右心衰竭甚至死亡,肺动脉高压与血液病关系密切,但目前未被血液科医生及时识别.本研究总结了可能会引起肺高血压的血液系统疾病,如溶血性贫血、骨髓增殖性疾病、浆细胞疾病,相关肺动脉高压的治疗,阐述可能的发病机制及临床表现,旨在提高血液科医师对肺高血压的认识.%Pulmonary hypertension (PH) refers to high blood pressure within the pulmonary circulation, which is a kind of malignant pulmonary vascular disease with or without small pulmonary artery lesions, often causes right heart failure and even death. PH is closely related to a blood disease, but is not recognized in time by a hematologist. Reviewed in this study were blood diseases that might cause PH, such as hemolytic anemia, myeloproliferative diseases, plasma cell disease and treatment-related PH. Possible pathogenesis was also described, aiming at improving the hematologist's understanding of PH.
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