布-加综合征误诊为肝硬化1例并文献复习

摘要

目的 探讨布一加综合征(BCS)的临床特点及误诊原因.方法 报道我科收治的1例被误诊为肝硬化2年的BCS患者,复习国内外已发表的文献.结果 BCS 临床表现与阻塞部位和阻塞程度有关,血管造影是诊断的金标准,治疗方法包括内科保守治疗、介入治疗和手术治疗.结论 BCS临床表现差异很大,误诊率极高,临床工作中要仔细询问病史,及时行血管超声及血管造影检查.%Objective To explore the clinical features of Budd-Chiari syndrome (BCS)and the reasons for misdiagnosis. Methods One case of BCS that was misdiagnosed as hepatic cirrhosis for two years was reported,and the published literatures were reviewed. Results Clinical features of BCS related to the position and the degree of obstruction. Digital subtraction angiography ( DSA ) was the gold standard for diagnosis. The therapeutic methods include conservative treatment,interventional therapy and surgical operation. Conclusion Large variety in clinical features of BCS may lead to high rate of misdiagnosis. In clinical management,medical history should be carefully taken,and vascular ultrasonography and DSA should be performed in a timely manner.