颞骨朗格汉斯细胞组织细胞增生症一例报道

摘要

Langerhans cell histiocytosis,a rare disease,often occurs in skull,pelvis,ribs etc. The literatures re-porting it is not many at home or abroad. This paper reported 1 case of langerhans cell histiocytosis in temporal bone and intro-duces its clinical features,imaging findings,pathological characteristics,treatment and prognosis to improve physicians' knowl-edge about it.%朗格汉斯细胞组织细胞增生症是一种较罕见的疾病，目前国内外文献报道较少。该病最常见的发病部位为骨骼，如颅骨、盆骨、肋骨等。本文结合1例发生在颞骨的朗格汉斯细胞组织细胞增生症患者的临床资料，就该病的临床特征、影像学表现、病理特点以及治疗和预后情况进行介绍，以期加强临床医师对该病的认识。