Use of N- (dibenz (b, f) oxepin-10-ylmethyl) -N-methyl-N-prop-2-ynylamine (OMIGAPIL) for the prophylaxis and / or treatment of congenital muscular dystrophy or myopathy due to collagen VI deficiency

摘要

The invention relates to the use of a compound of the formula (I) or a pharmaceutically acceptable addition salt thereof for the preparation of a medicament for the prophylaxis and/or treatment of muscular dystrophies or myopathies resulting from mutations in genes encoding for collagen VI.