Pancreatic neuroendocrine tumors may be functional or nonfunctional and solid or cystic. Cystic degeneration of neuroen-docrine tumors is uncommon because of the abundant vascular supply that characterizes these tumors, and nonfunctioning pancreatic cystic neuroendocrine tumors, as in this patient, are rare. Pancreatic cystic neuroendocrine tumors may arise spontaneously or in association with von Hippel-Lindau and Wermer syndromes. Computed tomography occasionally demonstrates the hypervascular border that is characteristic of neuroendocrine tumors, but EUS with FNA and immunocytology may be a more consistent means to establish the diagnosis. If the tumors are not diagnosed at an advanced stage, short- and long-term outcomes after resection are excellent.
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