Cogan's syndrome is a rare presumed autoimmune disorder characterized by nonsyphilitic interstitial keratitis and progressive audiovestibular symptoms. The initial report by David G. Cogan in 1945 was modified by Haynes et al in 1980 who proposed diagnostic criteria for patients with other ocular or vestibular symptoms and suggested this to be atypical Cogan's syndrome. In a more typical presentation of Cogan's syndrome, ocular and audiovestibular signs and symptoms usually appear alone and are bilateral. We report a case of 50-year-old woman with an atypical Cogan's syndrome manifested by unusual relatively rapid clinical deterioration.
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机译：科根综合症是一种罕见的假定的自身免疫性疾病，其特征为非梅毒间质性角膜炎和进行性听觉前庭症状。 1945年David G. Cogan的最初报告被Haynes等人在1980年修改，他们提出了具有其他眼部或前庭症状的患者的诊断标准，并认为这是非典型的Cogan综合征。在更典型的科根综合症表现中，眼和听觉前庭症状和体征通常单独出现且为双侧。我们报告了一例50岁的女性，具有非典型的相对较快的临床恶化表现出的非典型科根综合症。
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