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机译:奇瓦瓦河斑马鱼的骨材料质量严重受损,类似于经典的占优势人骨骨质骨质化不完全
Department of Osteology and BiomechanicsUniversity Medical Center Hamburg‐EppendorfHamburg Germany;
Department of Osteology and BiomechanicsUniversity Medical Center Hamburg‐EppendorfHamburg Germany;
Department of Osteology and BiomechanicsUniversity Medical Center Hamburg‐EppendorfHamburg Germany;
Department of Osteology and BiomechanicsUniversity Medical Center Hamburg‐EppendorfHamburg Germany;
Department of Osteology and BiomechanicsUniversity Medical Center Hamburg‐EppendorfHamburg Germany;
Department of Molecular MedicineUniversity of PaviaPavia Italy;
Department of Molecular MedicineUniversity of PaviaPavia Italy;
Carl Zeiss X‐ray MicroscopyPleasanton CA USA;
Department of Osteology and BiomechanicsUniversity Medical Center Hamburg‐EppendorfHamburg Germany;
Department of Molecular MedicineUniversity of PaviaPavia Italy;
Department of Molecular MedicineUniversity of PaviaPavia Italy;
Department of Osteology and BiomechanicsUniversity Medical Center Hamburg‐EppendorfHamburg Germany;
BONE HISTOMORPHOMETRY; GENETIC ANIMAL MODELS; BONE MATRIX; OSTEOGENESIS IMPERFECTA;
机译:奇瓦瓦河斑马鱼的骨材料质量严重受损,类似于经典的占优势人骨骨质骨质化不完全
机译:在成年子宫的子宫内移植可降低围产期致死率,并在敲除小鼠模型的经典显性成骨不全症中挽救骨表型。
机译:脯氨酰3-羟化酶1缺乏会导致隐性代谢性骨疾病,类似于致死/严重成骨不全症
机译:使用3D表征人成骨不全症中的骨管模式对CT图像进行分类
机译:人类生长激素的类胡萝卜素特异性表达提高转基因和成骨不全突变小鼠的骨质
机译:4PBA的分子伴侣活性改善了奇瓦瓦州的骨架表型奇瓦瓦州斑马鱼模型为显性成骨不全症
机译:奇瓦瓦河斑马鱼的骨材料质量严重受损类似于经典的占主导地位的人类骨质骨质化
机译:常染色体显性成骨不全中牙齿的扫描电子显微镜检查:支持遗传异质性