Enteritis Cystica Profunda Causing Intussusception (Case Report)

摘要

Enteritis Cystica Profunda (ECP) is a very rare benign disease entity of the small intestine. It is defined as mucin-f i I led cystic spaces, partially lined by non-neoplastic columnar to cuboidal or flattened epithelium found predominantly in the submucosa of the small bowel. We report a case of 12 year-old boy with small bowel intussusception caused by Enteritis Cystica Profunda. The patient had symptoms mimicking acute appendicitis except the passage of "red-currant jelly-like" diarrhea which drew attention to the possibility of intussusception which confirmed by ultrasonography. Diagnostic laparoscopy followed by laparoscopic assisted resection anastomosis of affected bowel which precipitated the intussusception. It contained a 2x2 cm mass intraluminally presenting the leading point of the intussusception, and proved histologi-caly as Enteritis Cystica Profunda. A review of the English medical literature revealed only four cases in children with similar symptoms in the last 32 years.