Systemic sclerosis sine scleroderma presenting as pulmonary intersticial fibrosis.

摘要

To the editor: Systemic sclerosis (SSc) is a generalized connective tissue disorder of unknown aetiology. The main types of SSc are diffuse cutaneous systemic sclerosis (dcSSc), limited cutaneous sclerosis systemic (lcSSc), systemic sclerosis sine scleroderma (ssSSc) and overlap syndromes . The ssSSc is a rare entity, scantly reported in the scientific literature , characterized by the absence of skin involvement. We present a case of a female diagnosed of ssSSc with pulmonary involvement.