Cardiac and gingival metastasis after total abdominal hysterectomy with bilateral salpingo-oophorectomy for primary uterine epithelioid angiosarcoma: case report and review of the literature

摘要

Uterine epithelioid angiosarcomas are extremely rare; only 24 cases have been documented worldwide. We present a unique case of cardiac and gingival metastases developing 4 years after total abdominal hysterectomy with bilateral salpingo-oophorectomy for primary uterine epithelial angiosarcoma. Initial treatment remains total abdominal hysterectomy with bilateral salpingo-oophorectomy. Limited distant metastases may be surgically resected in selected cases in order to improve quality of life or to prevent sudden death in untreated patients. Optimal chemotherapy regimens must be determined.