Gorlin-Goltz Syndrome: Case report and literature review

摘要

Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, with complete penetrance and variable expressivity, though sporadic cases have been described. This article includes a case report and an extensive review of the GGS with regard to its history, incidence, etiology, features, investigations, diagnostic criteria, keratocystic odontogenic tumor and treatment modalities.Keywords: Gorlin-Goltz syndrome, keratocystic odontogenic tumor, odontogenic keratocyst