Bilateral intracerebral hemorrhage as a presentation of central nervous system vasculitis in a patient with dermatomyositis

摘要

Primary CNSV diagnostic criteria includes: development of a neu- rological deficit unexplained by other processes; evidence of classic angiographic or histopathologic features of CNSV; and absence of any condition or systemic vasculitis that could elicit those features [1]. Intracerebral Hemorrhage (IH) is an uncommon manifestation in Cen- tral Nervous System Vasculitis (CNSV) [2,3]. The relationship between CNSV and Dermatomyositis is uncommon, and that is what makes the early diagnosis and appropriate treatment a challenge. We report a case of Dermatomyositis with bilateral IH and diagnosis of CNSV by angio- graphy.