Congenital Peribronchial Myofibroblastic Tumor: A Case Report and Review of the Literature

摘要

Background: Congenital peribronchial myofibroblastic tumor is a rare, solid mesenchymal tumor of the neonate, usually associated with non-immune hydrops fetalis. Case Report: We present a case of congenital peribronchial myofibroblastic tumor, in whom a right lung mass was detected in intrauterine life. 12 days after delivery by caesarean section, right lobectomy was performed. The tumor was limited to the lung, and was composed of spindle cells, proliferating around a bronchial unit. Central necrosis and 4-5 mitoses per 10 high power fields were present. The patient is well 26 months after surgery. Conclusion: We report this rare tumor with clinical, radiological and pathologic findings and a review of the literature. Turkish Ba?l?k: Konjenital Peribron?iyal Miyofibroblastik Tüm?r: Olgu Sunumu ve Literatürün G?zden Ge?irilmesi Anahtar Kelimeler: akci?er tüm?rü, konjenital, miyofibroblastik tüm?r Arkaplan: Konjenital peribron?iyal miyofibroblastik tüm?r neonatal d?nemin nadir, solid mezenkimal tüm?rü olup, s?kl?kla non-immün hidrops ile birliktedir. Olgu Sunumu: Sunulan olguda, intrauterin d?nemde sa? akci?erinde kitle saptanm?? ve do?umdan 12 gün sonra sa? lobektomi uygulanm??t?r. Tüm?r akci?ere s?n?rl? olup, bron?iyolleri ?evreleyerek ?o?alan i?si hücrelerden olu?maktayd?. Santral nekroz ve on büyük büyütme alan?nda d?rt-be? mitoz saptand?. Hasta cerrhi sonras? 20. ay?nda olup kontrollerinde sa?l?kl? seyretmektedir. Sonu?: Biz, nadir g?rülen bu tüm?rü klinik, radyolojik ve patolojik bulgular? ve literatürü g?zden ge?irerek sunmay? ama?lad?k.