Thymic carcinoid tumours, especially in the context of multiple endocrine neoplasia type 1 (MEN 1), present significant clinical challenges due to their rarity and aggressive nature. This case report describes a complex patient with MEN 1, who suffered from multiple manifestations of the disease, including thymic carcinoid. The tumour was initially resected and treated with adjuvant radiotherapy. Due to slow progression over the years, the tumour was treated with two lines of chemotherapy before the patient succumbed to progressive disease. There is currently limited evidence favoring any specific medical treatment for thymic carcinoid.
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机译:胸腺类癌瘤,尤其是在 1 型多发性内分泌腺瘤 (MEN 1) 的情况下,由于其罕见性和侵袭性,带来了重大的临床挑战。本病例报告描述了一名复杂的 MEN 1 患者,他患有多种疾病表现,包括胸腺类癌。最初切除肿瘤并接受辅助放疗。由于多年来进展缓慢,肿瘤在患者死于进行性疾病之前接受了两种化疗。目前支持胸腺类癌的任何特定药物治疗的证据有限。
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