Ventriculoatrial malalignment in atrioventricular septal defect resulting in uniatrial biventricular connection: surgical options

摘要

Apical 4-chamber view in patient 1 shows absent left atrioventricular connection, UBC, hypoplastic right ventricle and a solitary atrioventricular valve straddling a large inlet VSD ( ). The subcostal LAO-view ( ) shows the morphology of a common atrioventricular valve with a superior bridging leaflet (arrow) inserting to the right of the ventricular septum (asterix)