首页> 美国卫生研究院文献>Journal of Medical Ultrasound >Clinical and Echocardiography Features of Diagnosed in Adulthood Isolated Left Ventricular Noncompaction: A Case Series Study
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Clinical and Echocardiography Features of Diagnosed in Adulthood Isolated Left Ventricular Noncompaction: A Case Series Study

机译:成人成年孤立性左心室非紧致症的临床和超声心动图特征:病例系列研究

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摘要

Background:Left ventricular noncompaction cardiomyopathy (LVNC) is a primary genetic cardiomyopathy with morphologically unique characteristics, including loose “spongy” meshwork. Subjects carrying these disorders were typically presented with triad of heart failure, cardiac arrhythmias, and consequences of mural thrombi formation. The clinical and echocardiographic features regarding LVNC, however, are not widely known.
机译:背景:左室非紧凑型心肌病(LVNC)是一种原发性遗传性心肌病,具有形态独特的特征,包括松散的“海绵状”网状结构。患有这些疾病的受试者通常表现为心力衰竭,心脏心律不齐和壁血栓形成后果的三联征。然而,关于LVNC的临床和超声心动图特征尚不广泛。

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