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Isolated large vessel pulmonary vasculitis leading to pulmonary artery aneurysm formation: a case report and literature review

机译:孤立性大血管肺血管炎导致肺动脉瘤形成:一例病例报告并文献复习

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摘要

Pulmonary artery (PA) vasculitis occurs in association with primary vasculitides—in particular, giant cell arteritis, Takayasu’s arteritis, or Behçet’s disease—or secondary vasculitis as a result of infections or malignancy. However, PA vasculitis in isolation and with concomitant aneurysmal dilation is an unusual finding. We present a rare case of PA aneurysm secondary to isolated PA vasculitis in an asymptomatic patient with no features of systemic vasculitis. This case highlights one of the first cases of PA vasculitis managed with surgical resection alone.
机译:由于感染或恶性肿瘤,肺动脉(PA)血管炎与原发性血管炎(尤其是巨细胞性动脉炎,Takayasu的动脉炎或Behçet病)或继发性血管炎相关。然而,孤立的PA血管炎并伴有动脉瘤扩张是一个不寻常的发现。我们介绍了无症状患者无系统性血管炎的继发于孤立的PA血管炎的PA动脉瘤的罕见病例。该病例突出显示了仅通过手术切除即可治疗的首批PA血管炎。

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