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Essential Thrombocytosis-Associated Thromboembolism in the Abdominal Aorta

机译:腹主动脉血栓形成相关的血栓栓塞

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摘要

Essential thrombocytosis (ET) is a myeloproliferative disorder characterized by an anomalous increase in platelet production. Many patients with ET are asymptomatic. Few studies have reported ET-associated thromboembolism in large vessels such as the aorta. We report a patient with ET who presented with peripheral embolism from an abdominal aortic thrombus and developed acute limb ischemia. The patient underwent aortic replacement successfully. The patient’s platelet count was controlled with hydroxyurea, and no recurrence was noted over 2 years of follow-up.
机译:原发性血小板增多症(ET)是一种骨髓增生性疾病,其特征是血小板生成异常增加。许多ET患者无症状。很少有研究报道在大血管(例如主动脉)中与ET相关的血栓栓塞。我们报道了一名ET患者,该患者出现了来自腹主动脉血栓的周围栓塞并发展为急性肢体缺血。该患者成功接受了主动脉置换术。患者的血小板计数由羟基脲控制,在随访的2年中未发现复发。

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