Aphallia is an exceedingly rare congenital malformation. The condition is the result of a sporadic anatomic anomaly during fetal development in a 46, XY male patient with otherwise normal functioning testes and male sexual hormone metabolism. Neophallus reconstruction using the De Castro phalloplasty technique is currently the most accepted treatment modality for this condition. However, most case reports in the literature do not use tissue expansion. To achieve a larger neophallus and possibly decrease the need for secondary phalloplasty postpuberty, tissue expansion should be a standardized adjunct to the De Castro procedure in the management of all patients with congenital aphallia.
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机译:阳家菌是一种极其罕见的先天性畸形。这种情况是 46 岁 XY 岁男性患者在胎儿发育过程中散发解剖异常的结果,其他方面睾丸功能和男性性激素代谢正常。使用 De Castro成形术技术进行新重建是目前最被接受的这种情况的治疗方式。然而,文献中的大多数病例报告都没有使用组织扩增。为了获得更大的新并可能减少青春期后对二次成形术的需求,组织扩张应成为 De Castro 手术治疗所有先天性患者的标准化辅助手段。
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