目的 探讨肾脏原发性恶性纤维组织细胞瘤(MFH)的临床特点.方法 总结我院2002～2010年诊治的3例肾脏MFH患者的临床资料,并结合文献进行讨论.3例患者以血尿、腰痛、消瘦、发热就诊,均行手术治疗,术后病检确诊为肾脏MFH.结果 2例患者术后随访3个月、9个月死于肺转移,另1例患者随访6个月未见异常.结论 肾脏MFH罕见,恶性程度高,预后差.该病术前诊断困难,确诊主要依靠病理和免疫组化检查.治疗以早期手术为主,辅助治疗还值得进一步探讨.%Objective To investigate the clinical manifestation of renal primary malignant fibrous histiocytoma(MFH) . Methods 3 cases of renal MFH in our hospital were analyzed and summarized. Hematuria , emaciation,palpable mass were the common symptoms of renal MFH. Imaging features were not typical compared with other renal carcinomas . Immunohistiochemical test was essential for the diagnosis of renal MFH. All cases underwent surgical excision. Results Two patients were diagnosed of lung metastasis 3 and 9 months after the operation respectively. Conclusions Renal MFS is a rare pathological entity, it is highly agreessively with poor prognosis, surgery Diagnosis depends on pathology and Immunohistochemical methods. Early radical surgery is by now the optimal treatment.
展开▼
