脾脏硬化性血管瘤样结节性转化诊治(附1例报道及相关文献复习)

摘要

目的 探讨脾脏硬化性血管瘤样结节性转化(sclerosing angiomatoid nodular transformation,SANT)的诊断及治疗,提高对SANT的认识,避免误诊.方法 报道1例SANT的诊治过程并复习相关文献.结果 SANT是一种近年报道的罕见疾病,因临床表现及影像学检查无特异性,极易误诊,确诊需依赖其特征性的病理学形态及免疫组织化学染色.结论 SANT是一种罕见的良性病变,预后良好,行脾切除术可治愈.%Objective To explore the diagnoses and therapy of sclerosing angiomatoid nodular transformation to help us to deepen the understanding of it. Methods One case of SANT are reported and correlative other 30 cases of correlative literature are reviewed. Results SANT is a rare disease which is reported recent years. Because of lacking characteristic clinical course and ra-diologic features, it is often misdiagnosed, histological appearance and immunohistochemical staining are essential to clarify the diagnosis. Contusion SANT is a benign change in the spleen,which has a favourable prognosis and can be cured by splenectomy.