胆管内乳头状黏液性肿瘤的临床表现与影像学特征研究进展

摘要

关于胰腺导管内乳头状黏液性肿瘤(IPMN-P)的研究已近30年,学术界对其已有比较系统地了解.近年发现的胆管内乳头状黏液性肿瘤(IPMN-B)与IPMN-P有相似的临床特征,学者们从临床表现、影像学特征等各方面对IPMN-B逐渐认识.本文总结了从2000年发现至今报道的一部分IPMN-B典型病例,其临床表现可为上腹不适、胆绞痛、黄疸、间歇性发热,甚至没有任何症状;影像学三联征为黏胆症、胆管扩张及胆管壁肿物.%Understanding on the intraductal papillary mucinous neoplasm of the pancreas (IPMN-P) has dramatically improved in the past three decades. A new disease named intraductal papillary mucinous neoplasm of the bile duct (IPMN-B) reported in recent years shares several similar clinical features with IPMN-P. The clinical manifestations and imaging characteristics of IPMN-B have been gradually recognized. This review summarizes some of the typical cases reported since 2000 and find that clinical manifestations of IPMN-B include epigastric discomfort,biliary colic,jaundice,intermittent fever,sometimes without any symptoms;imaging triads for IPMN-B are mucobilia,dilated bile duct,and bile duct mural nodule.