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THE USE OF PHARMACEUTICAL COMPOSITIONS COMPRISING TRIGLYCERIDES WITH SEVEN - CARBON FATTY ACID IN THE PREPARATION OF MEDICAMENTS FOR THE TREATMENT OF FATTY ACID METABOLIC DEFECT
THE USE OF PHARMACEUTICAL COMPOSITIONS COMPRISING TRIGLYCERIDES WITH SEVEN - CARBON FATTY ACID IN THE PREPARATION OF MEDICAMENTS FOR THE TREATMENT OF FATTY ACID METABOLIC DEFECT
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机译:含有甘油和七碳脂肪酸的药物组合物在制备脂肪酸代谢缺陷药物中的应用。
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摘要
A seven-carbon fatty acid, preferably n-heptanoic acid, has been identified as an excellent energy source for patients suffering from inherited metabolic disorders or acquired metabolic derangements, especially defects in long-chain fatty acid metabolism. A seven-carbon fatty acid can also be provided in a nutritional supplement for patients who need an increase in the energy production derived from fatty acid metabolism.
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