Autoimmune chronic pancreatitis with IgG4-related pancreatic pseudocyst in a patient undergoing total pancreatectomy followed by autologous islet transplantation: A case report

摘要

Autoimmune pancreatitis (AIP), a rare type of chronic pancreatitis, has been recognized as an IgG4-related pancreatic disease, and the International Association of Pancreatology presented a set of diagnostic criteria for AIP recently. Although patients with AIP have an excellent response to steroid therapy, a relapse rate of 92% within 3 years has been reported, suggesting the need for further treatment options.A total pancreatectomy with islet au-totransplantation (TP-IAT) is a promising approach for refractory chronic pancreatitis to relieve severe abdominal pain and preserve endocrine function.4 Here, we present a patient who was clinically diagnosed with AIP, was resistant to steroid therapy, and underwent TP-IAT.