Management of a patient with mounier-kuhn syndrome undergoing repeated general anesthetics

摘要

Mounier-Kuhn syndrome (MKS) is characterized by tracheal and bronchial dilatation and tracheobronchomeg-aly. The clinical presentation varies widely from minimal respiratory discomfort, repetitive respiratory infections, mucus accumulation, and ineffective cough to severe respiratory failure.1"3 Airway management in these patients can be complicated by "air loss" during ventilation, resulting in hypoventilation and large airway collapse. There is also a high risk of aspiration because the cuff of the endotracheal tube (ETT) does not adhere to the tracheal mucosa and an airtight seal is not possible. We describe airway management in a MKS patient having repeated general anesthetics. The patient gave written consent for publication of this case.