Primary pancreatic sarcoma with liver metastases: Is there a place for radical surgery? [Sarcome primitif du pancréas avec métastases hépatiques: Place d'une chirurgie radicale?]

摘要

Pancreatic leiomyosarcomas are a rare neoplasm that accounts for 1/1000 of pancreatic cancers. In the literature, 23 cases of pancreatic leiomyosarcoma have been reported and the majority being diagnosed on autopsy [1]. It has never been reported any radical curative surgery in presence of synchronous hepatic metastasis [2]. We reported a case of a patient affected by a primitive pancreatic leiomyosarcoma with bilobar hepatic metastasis, who underwent distal splenopancreatectomy associated with the resection of multiples liver metastases.