Sudden cardiac death resulting from acute coronary artery aneurysm occlusion: successful resuscitation and treatment of an adolescent boy with previously unrecognized Kawasaki disease.

摘要

Kawasaki disease (mucocutaneous lymph node syndrome) is an inflammatory vasculitis of unknown etiology1'2 that is the most common cause of acquired coronary artery disease in children between 6 months and 5 years of age.3 Kawasaki disease is also the leading cause of acquired pediatric heart disease in the United States, exceeding rheumatic heart disease.4 Originally described5 and most common in Japan, Kawasaki disease is more prevalent in children of Asian or Pacific Island extraction compared with those of African-American or White decent.6 The disease affects boys more frequently than girls, occurs before the age of 5 years in more than three-quarters of affected children, and carries an overall mortality rate of approximately 0.17%.