An Extremely Rare Association of Posterior Fossa Arachnoid Cyst with Chiari I Malformation and Syringomyelia in a Child: A Short Report

摘要

Arachnoid cysts are benign, congenital, intra-arachnoid lesions. Posterior fossa arachnoid cyst associated with Chiari I malformation and syringomyelia is rare with none reported in children [1-3, 5-9]. Authors report the first of such an association in a 5-year-old child. A 5-year-old boy presented with suboc-cipital headache, neck pain and mild gait disturbance of 6 months’ duration. Neurological examination was unremarkable. He had undergone ventroperitoneal shunting 2 years previously at the referring hospital. MRI revealed a supracerebellar arachnoid cyst with severe tonsillar herniation up to the C_3 level and C_7-T_(10) level syringomyelia. Ventricles were adequately decompressed, and there was no communication of the cyst with the fourth ventricle (fig. la-c). Dynamic radiographs of the craniovertebral junction ruled out any bony instability.