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机译:GRIA2,MIR-409和MIR-495之间的调节电路受ESC衍生的运动神经元中的ALS FUS突变的影响
Center for Life Nano Science@Sapienza Istituto Italiano di Tecnologia;
Department of Biology and Biotechnology Sapienza University of Rome;
Department of Neurology Center for Motor Neuron Biology and Disease Columbia University;
Center for Life Nano Science@Sapienza Istituto Italiano di Tecnologia;
Center for Life Nano Science@Sapienza Istituto Italiano di Tecnologia;
Center for Life Nano Science@Sapienza Istituto Italiano di Tecnologia;
Department of Biology and Biotechnology Sapienza University of Rome;
Department of Neurology Center for Motor Neuron Biology and Disease Columbia University;
Institute of Molecular Biology and Pathology CNR;
Center for Life Nano Science@Sapienza Istituto Italiano di Tecnologia;
Center for Life Nano Science@Sapienza Istituto Italiano di Tecnologia;
ALS; FUS; RNA binding proteins; Motor neurons; Gria2; Excitotoxicity; MicroRNAs;
机译:GRIA2,MIR-409和MIR-495之间的调节电路受ESC衍生的运动神经元中的ALS FUS突变的影响
机译:FUS 3'-UTR中与ALS相关的突变破坏了microRNA–FUS调控电路
机译:来自ALS患者的C9ORF72,FUS,SOD1或TDP43突变的IPSC衍生的运动神经元中的钙动力学和谷氨酸受体特性改变了钙动力学和谷氨酸受体特性
机译:皮质螺旋运动神经元电路的分子发育1
机译:用ESC衍生的颅和脊髓运动神经元建模ALS差异性脆弱性
机译:U1 snRNP在FUS中携带NLS突变的ALS患者成纤维细胞中定位错误是斑马鱼运动神经元向外生长所必需的
机译:GRIA2,MIR-409和MIR-495之间的调节电路受ESC衍生的运动神经元中的ALS FUS突变的影响