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机译:Nemo和Sharpin之间缺乏相互作用损害线性泛素和NF-κB活化,并导致失禁的Pigmenti
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
Laboratory of Signaling and Pathogenesis CNRS UMR 3691 Pasteur Institute;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
Departments of Cell Biology and Infection and of Structural Biology and Chemistry URA 2185;
Rockefeller Branch St Giles Laboratory of Human Genetics of Infectious Diseases Rockefeller;
Institute of Genetics and Biophysics “Adriano Buzzati-Traverso” (CNR);
Rockefeller Branch St Giles Laboratory of Human Genetics of Infectious Diseases Rockefeller;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
Institute of Genetics and Biophysics “Adriano Buzzati-Traverso” (CNR);
Department of Dermatology Dijon CHU Medicine Faculty and Bourgogne University EA427 Genetic of;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
Rockefeller Branch St Giles Laboratory of Human Genetics of Infectious Diseases Rockefeller;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
Laboratory of Signaling and Pathogenesis CNRS UMR 3691 Pasteur Institute;
Departments of Cell Biology and Infection and of Structural Biology and Chemistry URA 2185;
INSERM U1163 Paris-Descartes University Sorbonne Paris Cité IMAGINE Institute Necker Hospital;
Incontinentia pigmenti; IKBKG; NF-築 essential modulator; nuclear factor 築; linear ubiquitin assembly complex; linear ubiquitination; SHANK-associated RH domaininteracting protein;
机译:Nemo和Sharpin之间缺乏相互作用损害线性泛素和NF-κB活化,并导致失禁的Pigmenti
机译:IKBKG中新的亚型突变会损害NEMO泛素化,导致外胚层发育异常,免疫缺陷,色素失禁和免疫性血小板减少性紫癜
机译:通过分析导致色素失禁的新NEMO突变来鉴定TRAF6依赖性NEMO多泛素化位点
机译:质谱测量检测NEMO上的Sharpin依赖性线性泛粘性
机译:韩国色素性尿失禁患者常见的NF-κB必需调节剂(NEMO)基因重排
机译:Nemo和Sharpin之间缺乏相互作用损害线性泛素和NF-κB活化,并导致失禁的Pigmenti