Klippel-Trenaunay-Weber Syndrome

摘要

The parents of this 2-year-old boy brought their son for evaluation of swelling of the right leg and excoriation and serosanguineous discharge from the ankle region of 3 days' duration. The child had had a hemangioma of the right ankle since birth. Subsequently, there was gradual spread of the lesion along the leg to the buttocks.This patient had Klippel-Trenaunay-Weber syndrome with secondary celluli-tis of the leg.Hemangiomas are common in infancy and are often benign. Klippel-Trenaunay-Weber syndrome is characterized by the triad of capillary and venous malformations, venous varicos-ity, and hyperplasia of soft tissue in the affected area. Parkes Weber syndrome is diagnosed when this triad is accompanied by an arteriovenous fistula.