A Child with Intra-orbital Oculomotor Nerve Schwannoma without Neurofibromatosis

摘要

Orbital tumors constitute a heterogeneous array of lesions and pose numerous challenges in terms of diagnosis, imaging and treatment. The bony orbit contains an extremely complicated anatomical architecture composed of II, III, IV, VI cranial nerves, vessels, extra ocular muscles and the globe. Schwannoma of cranial nerves represent less than 8% of all intracranial neoplasms usually arising from the vestibulocochlear nerve. These tumors are commonly seen in association, with Neurofibromatosis and constitute approximately 1% of all orbital tumors. To date there are only 38 reported cases of orbital tumors arising from the oculomotor nerve, and only four arising within the orbit.