Fludrocortisone in the Management of an Infant with a Single Ventricle and an Overly Tightened Pulmonary Artery Band

摘要

We describe a 2-month-old female infant with a univentricular heart and overly tightened pulmonary artery band (PAB) resulting in hypercyanotic episodes. Despite adequate doses of morphine and a beta-blocker, she continued to have multiple hypercyanotic events per day. Treatment with fludrocortisone resulted in resolution of these episodes and allowed performance of a Glenn shunt at 3 half months of age. We conclude that fludrocortisone may be beneficial in the management of an overly tightened PAB until the patient is suitable for surgical intervention.