Successful Staged Neonatal Repair of Tetralogy of Fallot with Long-Segment Hypoplasia of the Aorta

摘要

We describe an extremely rare combination of tetralogy of Fallot (TOF), right-sided cervical aortic arch with long-segment hypoplasia, and other vascular anomalies. A two-stage surgical approach included aortic arch reconstruction followed by right ventricular muscle bundle division and ventricular septal defect closure a few weeks later. The initial clinical presentation, perioperative course, and imaging studies are presented along with a review of the relevant literature. This is the first report of successful neonatal repair of TOF with long-segment hypoplasia of the aorta. Keywords Aortic arch hypoplasia - Coarctation - Interrupted aortic arch - Neonatal repair - Tetralogy of Fallot Jimmy C. Lu and Sanket S. Shah contributed equally to this work.